ICD-10-CM (2010)/CHAPTER 6

Diseases of the nervous system (G00-G99)

Excludes2: certain conditions originating in the perinatal period (P04-P96)

certain infectious and parasitic diseases (A00-B99)

complications of pregnancy, childbirth and the puerperium (O00-O99)

congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)

endocrine, nutritional and metabolic diseases (E00-E90)

injury, poisoning and certain other consequences of external causes (S00-T98)

neoplasms (C00-D48)

symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)

This chapter contains the following blocks:

G00-G09 Inflammatory diseases of the central nervous system

G10-G14 Systemic atrophies primarily affecting the central nervous system

G20-G26 Extrapyramidal and movement disorders

G30-G32 Other degenerative diseases of the nervous system

G35-G37 Demyelinating diseases of the central nervous system

G40-G47 Episodic and paroxysmal disorders

G50-G59 Nerve, nerve root and plexus disorders

G60-G64 Polyneuropathies and other disorders of the peripheral nervous system

G70-G73 Diseases of myoneural junction and muscle

G80-G83 Cerebral palsy and other paralytic syndromes

G89-G99 Other disorders of the nervous system

=Inflammatory diseases of the central nervous system (G00-G09) =

G00 Bacterial meningitis, not elsewhere classified

Includes bacterial arachnoiditis

bacterial leptomeningitis

bacterial meningitis

bacterial pachymeningitis

Excludes1: bacterial:

meningoencephalitis (G04.2)

meningomyelitis (G04.2)

G00.0 Hemophilus meningitis

Meningitis due to Hemophilus influenzae

G00.1 Pneumococcal meningitis

G00.2 Streptococcal meningitis

Use additional code to further identify organism (B95.0-B95.5)

G00.3 Staphylococcal meningitis

Use additional code to further identify organism (B95.6-B95.8)

G00.8 Other bacterial meningitis

Meningitis due to Escherichia coli

Meningitis due to Friedl?nder bacillus

Meningitis due to Klebsiella

Use additional code to further identify organism (B96.-)

G00.9 Bacterial meningitis, unspecified

Meningitis due to gram-negative bacteria, unspecified

Purulent meningitis NOS

Pyogenic meningitis NOS

Suppurative meningitis NOS

G01 Meningitis in bacterial diseases classified elsewhere

Code first underlying disease

Excludes1: meningitis (in):

gonococcal (A54.81)

leptospirosis (A27.81)

listeriosis (A32.11)

Lyme disease (A69.21)

meningococcal (A39.0)

neurosyphilis (A52.13)

tuberculosis (A17.0)

meningoencephalitis and meningomyelitis in bacterial diseases classified elsewhere (G05)

G02 Meningitis in other infectious and parasitic diseases classified elsewhere

Code first underlying disease, such as:

poliovirus infection (A80.-)

Excludes1: meningitis (due to):

candidal (B37.5)

coccidioidomycosis (B38.4)

cryptococcal meningitis (B45.1)

herpesviral [herpes simplex] (B00.3)

infectious mononucleosis (B27.-2)

measles (B05.1)

mumps (B26.1)

rubella (B06.02)

varicella [chickenpox] (B01.0)

zoster (B02.1)

meningoencephalitis and meningomyelitis in other infectious and parasitic diseases classified elsewhere (G05)

G03 Meningitis due to other and unspecified causes

Includes arachnoiditis NOS

leptomeningitis NOS

meningitis NOS

pachymeningitis NOS

Excludes1: meningoencephalitis (G04.-)

meningomyelitis (G04.-)

G03.0 Nonpyogenic meningitis

Aseptic meningitis

Nonbacterial meningitis

G03.1 Chronic meningitis

G03.2 Benign recurrent meningitis [Mollaret]

G03.8 Meningitis due to other specified causes

G03.9 Meningitis, unspecified

Arachnoiditis (spinal) NOS

G04 Encephalitis, myelitis and encephalomyelitis

Includes acute ascending myelitis

meningoencephalitis

meningomyelitis

Excludes1: encephalopathy NOS (G93.40)

Excludes2: acute transverse myelitis (G37.3-)

alcoholic encephalopathy (G31.2)

benign myalgic encephalomyelitis (G93.3)

multiple sclerosis (G35)

subacute necrotizing myelitis (G37.4)

toxic encephalitis (G92)

toxic encephalopathy (G92)

G04.0 Acute disseminated encephalitis and encephalomyelitis (ADEM)

Excludes1: acute necrotizing hemorrhagic encephalopathy (G04.3-)

G04. 00 Postinfectious acute disseminated encephalitis and encephalomyelitis (postinfectious ADEM)

Acute disseminated encephalitis and encephalomyelitis NOS

Excludes1: noninfectious acute disseminated encephalomyelitis (noninfectious ADEM) (G04.81)

postchickenpox encephalitis (B01.1)

postmeasles encephalitis (B05.0)

postmeasles myelitis (B05.1)

G04.01 Postimmunization acute disseminated encephalitis, myelitis and encephalomyelitis

Encephalitis, postimmunization

Encephalomyelitis, postimmunization

Use additional code to identify the vaccine (T50.A-, T50.B-, T50.Z-)

G04.1 Tropical spastic paraplegia

G04.2 Bacterial meningoencephalitis and meningomyelitis, not elsewhere classified

G04.3 Acute necrotizing hemorrhagic encephalopathy

Excludes1: acute disseminated encephalitis and encephalomyelitis (G04.0-)

G04.30 Postinfectious acute necrotizing hemorrhagic encephalopathy

Acute necrotizing hemorrhagic encephalopathy NOS

G04.31 Postimmunization acute necrotizing hemorrhagic encephalopathy

Use additional code to identify the vaccine (T50.A-, T50.B-, T50.Z-)

G04.8 Other encephalitis, myelitis and encephalomyelitis

G04.81 Other encephalitis and encephalomyelitis

Noninfectious acute disseminated encephalomyelitis (noninfectious ADEM)

G04.89 Other myelitis

G04.9 Encephalitis, myelitis and encephalomyelitis, unspecified

G04.90 Encephalitis and encephalomyelitis, unspecified

Ventriculitis (cerebral) NOS

G04.91 Myelitis, unspecified

G05 Encephalitis, myelitis and encephalomyelitis in diseases classified elsewhere

Code first underlying disease, such as:

poliovirus (A80.-)

suppurative otitis media (H66.01-H66.4)

trichinellosis (B75)

Excludes1: encephalitis, myelitis and encephalomyelitis (in):

adenoviral ( A85.1)

cytomegaloviral (B25.8)

enteroviral (A85.0)

herpesviral [herpes simplex] (B00.4)

listerial (A32.12)

measles (B05.0)

meningococcal (A39.81)

mumps (B26.2)

postchickenpox (B01.1)

rubella (B06.01)

systemic lupus erythematosus (M32.19)

toxoplasmosis (B58.2)

congenital (P37.1)

zoster (B02.0)

eosinophilic meningoencephalitis (B83.2)

G05.3 Encephalitis and encephalomyelitis in diseases classified elsewhere

Meningoencephalitis in diseases classified elsewhere

G05.4 Myelitis in diseases classified elsewhere

Meningomyelitis in diseases classified elsewhere

G06 Intracranial and intraspinal abscess and granuloma

Use additional code (B95-B97) to identify infectious agent.

G06.0 Intracranial abscess and granuloma

Brain [any part] abscess (embolic)

Cerebellar abscess (embolic)

Cerebral abscess (embolic)

Intracranial epidural abscess or granuloma

Intracranial extradural abscess or granuloma

Intracranial subdural abscess or granuloma

Otogenic abscess (embolic)

Excludes1: tuberculous intracranial abscess and granuloma (A17.81)

G06.1 Intraspinal abscess and granuloma

Abscess (embolic) of spinal cord [any part]

Intraspinal epidural abscess or granuloma

Intraspinal extradural abscess or granuloma

Intraspinal subdural abscess or granuloma

Excludes1: tuberculous intraspinal abscess and granuloma (A17.81)

G06.2 Extradural and subdural abscess, unspecified

G07 Intracranial and intraspinal abscess and granuloma in diseases classified elsewhere

Code first, underlying disease, such as:

schistosomiasis granuloma of brain (B65.-)

Excludes1: abscess of brain:

amebic (A06.6)

chromomycotic (B43.1)

gonococcal (A54.82)

tuberculous ( A17.81)

tuberculoma of meninges (A17.1)

G08 Intracranial and intraspinal phlebitis and thrombophlebitis

Includes septic embolism of intracranial or intraspinal venous sinuses and veins

septic endophlebitis of intracranial or intraspinal venous sinuses and veins

septic phlebitis of intracranial or intraspinal venous sinuses and veins

septic thrombophlebitis of intracranial or intraspinal venous sinuses and veins

septic thrombosis of intracranial or intraspinal venous sinuses and veins

Excludes1: intracranial phlebitis and thrombophlebitis complicating:

abortion, ectopic or molar pregnancy (O00-O07, O08.7)

pregnancy, childbirth and the puerperium (O22.5, O87.3)

nonpyogenic intracranial phlebitis and thrombophlebitis (I67.6)

nonpyogenic intraspinal phlebitis and thrombophlebitis (G95.1)

G09 Sequelae of inflammatory diseases of central nervous system

Note: Category G09 is to be used to indicate conditions whose primary classification is to G00-G08 as the cause of sequelae, themselves classifiable elsewhere. The "sequelae" include conditions specified as residuals.

Code first condition resulting from (sequela) of inflammatory diseases of central nervous system

Systemic atrophies primarily affecting the central nervous system (G10-G14)

G10 Huntington's disease

Includes Huntington's chorea

Huntington's dementia

G11 Hereditary ataxia

Excludes2: cerebral palsy (G80.-)

hereditary and idiopathic neuropathy (G60.-)

metabolic disorders (E70-E90)

G11.0 Congenital nonprogressive ataxia

G11.1 Early-onset cerebellar ataxia

Early-onset cerebellar ataxia with essential tremor

Early-onset cerebellar ataxia with myoclonus [Hunt's ataxia]

Early-onset cerebellar ataxia with retained tendon reflexes

Friedreich's ataxia (autosomal recessive)

X-linked recessive spinocerebellar ataxia

G11. 2 Late-onset cerebellar ataxia

G11.3 Cerebellar ataxia with defective DNA repair

Ataxia telangiectasia [Louis-Bar]

Excludes2: Cockayne's syndrome (Q87.1)

other disorders of purine and pyrimidine metabolism (E79.-)

xeroderma pigmentosum (Q82.1)

G11.4 Hereditary spastic paraplegia

G11.8 Other hereditary ataxias

G11.9 Hereditary ataxia, unspecified

Hereditary cerebellar ataxia NOS

Hereditary cerebellar degeneration

Hereditary cerebellar disease

Hereditary cerebellar syndrome

G12 Spinal muscular atrophy and related syndromes

G12.0 Infantile spinal muscular atrophy, type I [Werdnig-Hoffman]

G12.1 Other inherited spinal muscular atrophy

Adult form spinal muscular atrophy

Childhood form, type II spinal muscular atrophy

Distal spinal muscular atrophy

Juvenile form, type III spinal muscular atrophy [Kugelberg-Welander]

Progressive bulbar palsy of childhood [Fazio-Londe]

Scapuloperoneal form spinal muscular atrophy

G12.2 Motor neuron disease

G12.20 Motor neuron disease, unspecified

G12.21 Amyotrophic lateral sclerosis

Progressive spinal muscle atrophy

G12.22 Progressive bulbar palsy

G12.29 Other motor neuron disease

Familial motor neuron disease

Primary lateral sclerosis

G12.8 Other spinal muscular atrophies and related syndromes

G12.9 Spinal muscular atrophy, unspecified

G13 Systemic atrophies primarily affecting central nervous system in diseases classified elsewhere

G13.0 Paraneoplastic neuromyopathy and neuropathy

Carcinomatous neuromyopathy

Sensorial paraneoplastic neuropathy [Denny Brown]

Code first underlying neoplasm (C00-D48)

G13.1 Other systemic atrophy primarily affecting central nervous system in neoplastic disease

Paraneoplastic limbic encephalopathy

Code first underlying neoplasm (C00-D48)

G13.8 Systemic atrophy primarily affecting central nervous system in other diseases classified elsewhere

Code first underlying disease, such as:

cerebellar ataxia (in):

hypothyroidism (E03.-)

myxedematous congenital iodine deficiency (E00.1)

G14 Postpolio syndrome

Postpolio myelitic syndrome

Excludes1: sequelae of poliomyelitis (B91)

Extrapyramidal and movement disorders (G20-G26)

G20 Parkinson's disease

Includes hemiparkinsonism

idiopathic Parkinsonism or Parkinson's disease

paralysis agitans

Parkinsonism or Parkinson's disease NOS

primary Parkinsonism or Parkinson's disease

Excludes1: dementia with Parkinsonism (G31.83)

G21 Secondary parkinsonism

Excludes1: dementia with Parkinsonism (G31.83)

Huntington's disease (G10)

Shy-Drager syndrome (G90.3)

syphilitic Parkinsonism (A52.19)

G21.0 Malignant neuroleptic syndrome

Code first (T43.3-T43.5) to identify drug

Excludes1: neuroleptic induced parkinsonism (G21.11)

G21.1 Other drug-induced secondary parkinsonism

G21.11 Neuroleptic induced parkinsonism

Code first (T43.3-T43.5) to identify drug

Excludes1: malignant neuroleptic syndrome (G21.0)

G21.19 Other drug induced secondary parkinsonism

Code first (T36-T50) to identify drug

G21.2 Secondary parkinsonism due to other external agents

Code first (T51-T65) to identify external agent

G21.3 Postencephalitic parkinsonism

G21.4 Vascular parkinsonism

G21.8 Other secondary parkinsonism

G21.9 Secondary parkinsonism, unspecified

G23 Other degenerative diseases of basal ganglia

Excludes2: multi-system degeneration of the autonomic nervous system (G90.3)

G23.0 Hallervorden-Spatz disease

Pigmentary pallidal degeneration

G23.1 Progressive supranuclear ophthalmoplegia [Steele-Richardson-Olszewski]

G23.2 Striatonigral degeneration

G23. 8 Other specified degenerative diseases of basal ganglia

Calcification of basal ganglia

G23.9 Degenerative disease of basal ganglia, unspecified

G24 Dystonia

Includes dyskinesia

Excludes2: athetoid cerebral palsy (G80.3)

G24.0 Drug induced dystonia

Code first (T36-T50) to identify drug

G24.01 Drug induced subacute dyskinesia

Drug induced blepharospasm

Drug induced orofacial dyskinesia

Neuroleptic induced tardive dyskinesia

Tardive dyskinesia

G24.02 Drug induced acute dystonia

Acute dystonic reaction to drugs

Neuroleptic induced acute dystonia

G24.09 Other drug induced dystonia

G24.1 Genetic torsion dystonia

Dystonia deformans progressiva

Dystonia musculorum deformans

Familial torsion dystonia

Idiopathic familial dystonia

Idiopathic (torsion) dystonia NOS

(Schwalbe-) Ziehen-Oppenheim disease

G24.2 Idiopathic nonfamilial dystonia

G24.3 Spasmodic torticollis

Excludes1: congenital torticollis (Q68.0)

hysterical torticollis (F44.4)

ocular torticollis (R29.891)

psychogenic torticollis (F45.8)

torticollis NOS (M43.6)

traumatic recurrent torticollis (S13.4)

G24.4 Idiopathic orofacial dystonia

Orofacial dyskinesia

Excludes1: drug induced orofacial dyskinesia (G24.01)

G24.5 Blepharospasm

Excludes1: drug induced blepharospasm (G24.01)

G24.8 Other dystonia

Acquired torsion dystonia NOS

G24.9 Dystonia, unspecified

Dyskinesia NOS

G25 Other extrapyramidal and movement disorders

Excludes2: sleep related movement disorders (G47.6-)

G25.0 Essential tremor

Familial tremor

Excludes1: tremor NOS (R25.1)

G25.1 Drug-induced tremor

Code first (T36-T50) to identify drug

G25.2 Other specified forms of tremor

Intention tremor

G25.3 Myoclonus

Drug-induced myoclonus

Palatal myoclonus

Code first (T36-T50) to identify drug, if drug-induced

Excludes1: facial myokymia (G51.4)

myoclonic epilepsy (G40.-)

G25.4 Drug-induced chorea

Code first (T36-T50) to identify drug

G25.5 Other chorea

Chorea NOS

Excludes1: chorea NOS with heart involvement (I02.0)

Huntington's chorea (G10)

rheumatic chorea (I02.-)

Sydenham's chorea (I02.-)

G25.6 Drug induced tics and other tics of organic origin

G25.61 Drug induced tics

Code first (T36-T50) to identify drug

G25.69 Other tics of organic origin

Excludes1: habit spasm (F95.9)

tic NOS (F95.9)

Tourette?s syndrome (F95.2)

G25.7 Other and unspecified drug induced movement disorders

Code first (T36-T50) to identify drug

G25.70 Drug induced movement disorder, unspecified

G25.71 Drug induced akathisia

Drug induced acathisia

Neuroleptic induced acute akathisia

G25.79 Other drug induced movement disorders

G25.8 Other specified extrapyramidal and movement disorders

G25.81 Restless legs syndrome

G25.82 Stiff-man syndrome

G25.89 Other specified extrapyramidal and movement disorders

G25.9 Extrapyramidal and movement disorder, unspecified

G26 Extrapyramidal and movement disorders in diseases classified elsewhere

Code first underlying disease

Other degenerative diseases of the nervous system (G30-G32)

G30 Alzheimer's disease

Includes Alzheimer's dementia senile and presenile forms

Use additional code to identify:

delirium, if applicable (F05)

dementia with behavioral disturbance (F02.81)

dementia without behavioral disturbance (F02.80)

Excludes1: senile degeneration of brain NEC (G31.1)

senile dementia NOS (F03)

senility NOS (R41.81)

G30.0 Alzheimer's disease with early onset

G30.1 Alzheimer's disease with late onset

G30.8 Other Alzheimer's disease

G30.9 Alzheimer's disease, unspecified

G31 Other degenerative diseases of nervous system, not elsewhere classified

Use additional code to identify:

dementia with behavioral disturbance (F02.81)

dementia without behavioral disturbance (F02.80)

Excludes2: Reye's syndrome (G93.7)

G31.0 Frontotemporal dementia

G31.01 Pick's disease

Circumscribed brain atrophy

Progressive isolated aphasia

G31.09 Other frontotemporal dementia

Frontal dementia

G31.1 Senile degeneration of brain, not elsewhere classified

Excludes1: Alzheimer's disease (G30.-)

senility NOS (R41.81)

G31.2 Degeneration of nervous system due to alcohol

Alcoholic cerebellar ataxia

Alcoholic cerebellar degeneration

Alcoholic cerebral degeneration

Alcoholic encephalopathy

Dysfunction of the autonomic nervous system due to alcohol

Code also associated alcoholism (F10.-)

G31.8 Other specified degenerative diseases of nervous system

G31.81 Alpers disease

Grey-matter degeneration

G31.82 Leigh's disease

Subacute necrotizing encephalopathy

G31.83 Dementia with Lewy bodies

Dementia with Parkinsonism

Lewy body dementia

Lewy body disease

G31.84 Mild cognitive impairment, so stated

Excludes1: age related cognitive decline (R41.81)

altered mental status (R41.82)

cerebral degeneration (G31.9)

change in mental status (R41.82)

cognitive deficits following (sequelae of) cerebral hemorrhage or infarction (I69.01, I69.11, I69.21, I69.31, I69.81, I69.91)

cognitive impairment due to intracranial or head injury (S06.-)

dementia (F01.-, F02.-, F03)

mild memory disturbance (F06.8)

neurologic neglect syndrome (R41.4)

personality change, nonpsychotic (F68.8)

G31.89 Other specified degenerative diseases of nervous system

G31.9 Degenerative disease of nervous system, unspecified

G32 Other degenerative disorders of nervous system in diseases classified elsewhere

G32.0 Subacute combined degeneration of spinal cord in diseases classified elsewhere

Dana-Putnam syndrome

Sclerosis of spinal cord (combined) (dorsolateral) (posterolateral)

Code first underlying disease, such as:

vitamin B12 deficiency (E53.8)

anemia (D51.9)

dietary (D51.3)

pernicious (D51.0)

Excludes1: syphilitic combined degeneration of spinal cord (A52.11)

G32.8 Other specified degenerative disorders of nervous system in diseases classified elsewhere

Degenerative encephalopathy in diseases classified elsewhere

Code first underlying disease, such as:

cerebral degeneration (due to):

amyloid (E85.-)

hypothyroidism (E00.-, E03.-)

neoplasm (C00-D48)

vitamin B deficiency, except thiamine (E52-E53.-)

Excludes1: superior hemorrhagic polioencephalitis [Wernicke's encephalopathy] (E51.2)

Demyelinating diseases of the central nervous system (G35-G37)

G35 Multiple sclerosis

Includes disseminated multiple sclerosis

generalized multiple sclerosis

multiple sclerosis NOS

multiple sclerosis of brain stem

multiple sclerosis of cord

G36 Other acute disseminated demyelination

Excludes1: postinfectious encephalitis and encephalomyelitis NOS (G04.020)

G36.0 Neuromyelitis optica [Devic]

Demyelination in optic neuritis

Excludes1: optic neuritis NOS (H46)

G36.1 Acute and subacute hemorrhagic leukoencephalitis [Hurst]

G36.8 Other specified acute disseminated demyelination

G36.9 Acute disseminated demyelination, unspecified

G37 Other demyelinating diseases of central nervous system

G37.0 Diffuse sclerosis of central nervous system

Periaxial encephalitis

Schilder's disease

Excludes1: X linked adrenoleukodystrophy (E71.42-)

G37.1 Central demyelination of corpus callosum

G37.2 Central pontine myelinolysis

G37.3 Acute transverse myelitis in demyelinating disease of central nervous system

Acute transverse myelitis NOS

Acute transverse myelopathy

Excludes1: multiple sclerosis (G35)

neuromyelitis optica [Devic] (G36.0)

G37.4 Subacute necrotizing myelitis of central nervous system

G37.5 Concentric sclerosis [Balo] of central nervous system

G37.8 Other specified demyelinating diseases of central nervous system

G37.9 Demyelinating disease of central nervous system, unspecified

Episodic and paroxysmal disorders (G40-G47)

G40 Epilepsy and recurrent seizures

Note: the following terms are to be considered equivalent to intractable: pharmacoresistant (pharmacologically resistant), treatment resistant, refractory (medically) and poorly controlled

Excludes1: conversion disorder with seizures (F44.5)

convulsions NOS (R56.9)

hippocampal sclerosis (G93.81)

Landau-Kleffner syndrome (F80.3)

mesial temporal sclerosis (G93.81)

seizure (convulsive) NOS (R56.9)

seizure of newborn (P90)

temporal sclerosis (G93.81)

Todd's paralysis (G83.8)

G40.0 Localization-related (focal) (partial) idiopathic epilepsy and epileptic syndromes with seizures of localized onset

Benign childhood epilepsy with centrotemporal EEG spikes

Childhood epilepsy with occipital EEG paroxysms

Excludes1: adult onset localization-related epilepsy (G40.1-, G40.2-)

G40.00 Localization-related (focal) (partial) idiopathic epilepsy and epileptic syndromes with seizures of localized onset, not intractable

Localization-related (focal) (partial) idiopathic epilepsy and epileptic syndromes with seizures of localized onset without intractability

G40.001 Localization-related (focal) (partial) idiopathic epilepsy and epileptic syndromes with seizures of localized onset, not intractable, with status epilepticus

G40.009 Localization-related (focal) (partial) idiopathic epilepsy and epileptic syndromes with seizures of localized onset, not intractable, without status epilepticus

Localization-related (focal) (partial) idiopathic epilepsy and epileptic syndromes with seizures of localized onset NOS

G40.01 Localization-related (focal) (partial) idiopathic epilepsy and epileptic syndromes with seizures of localized onset, intractable

G40.011 Localization-related (focal) (partial) idiopathic epilepsy and epileptic syndromes with seizures of localized onset, intractable, with status epilepticus

G40.019 Localization-related (focal) (partial) idiopathic epilepsy and epileptic syndromes with seizures of localized onset, intractable, without status epilepticus

G40.1 Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with simple partial seizures

Attacks without alteration of consciousness

Simple partial seizures developing into secondarily generalized seizures

G40.10 Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with simple partial seizures, not intractable

Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with simple partial seizures without intractability

G40.101 Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with simple partial seizures, not intractable, with status epilepticus

G40.109 Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with simple partial seizures, not intractable, without status epilepticus

Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with simple partial seizures NOS

G40.11 Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with simple partial seizures, intractable

G40.111 Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with simple partial seizures, intractable, with status epilepticus

G40.119 Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with simple partial seizures, intractable, without status epilepticus

G40.2 Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with complex partial seizures

Attacks with alteration of consciousness, often with automatisms

Complex partial seizures developing into secondarily generalized seizures

G40.20 Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with complex partial seizures, not intractable

Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with complex partial seizures without intractability

G40.201 Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with complex partial seizures, not intractable, with status epilepticus

G40.209 Localization-related (focal) (partial) symptomatic epilepsy and epileptic

syndromes with complex partial seizures, not intractable, without status epilepticus

Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with complex partial seizures NOS

G40.21 Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with complex partial seizures, intractable

G40.211 Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with complex partial seizures, intractable, with status epilepticus

G40.219 Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with complex partial seizures, intractable, without status epilepticus

G40.3 Generalized idiopathic epilepsy and epileptic syndromes

Benign myoclonic epilepsy in infancy

Benign neonatal convulsions (familial)

Childhood absence epilepsy [pyknolepsy]

Epilepsy with grand mal seizures on awakening

Grand mal seizure NOS

Juvenile absence epilepsy

Juvenile myoclonic epilepsy [impulsive petit mal]

Nonspecific atonic epileptic seizures

Nonspecific clonic epileptic seizures

Nonspecific myoclonic epileptic seizures

Nonspecific tonic epileptic seizures

Nonspecific tonic-clonic epileptic seizures

Petit mal seizure NOS

Code also: MERRF syndrome, if applicable, (M88.32)

G40.30 Generalized idiopathic epilepsy and epileptic syndromes, not intractable

Generalized idiopathic epilepsy and epileptic syndromes without intractability

G40.301 Generalized idiopathic epilepsy and epileptic syndromes, not intractable, with status epilepticus

G40.309 Generalized idiopathic epilepsy and epileptic syndromes, not intractable, without status epilepticus

Generalized idiopathic epilepsy and epileptic syndromes NOS

G40.31 Generalized idiopathic epilepsy and epileptic syndromes, intractable

G40. 311 Generalized idiopathic epilepsy and epileptic syndromes, intractable, with status epilepticus

G40.319 Generalized idiopathic epilepsy and epileptic syndromes, intractable, without status epilepticus

G40.4 Other generalized epilepsy and epileptic syndromes

Epilepsy with myoclonic absences

Epilepsy with myoclonic-astatic seizures

Infantile spasms

Lennox-Gastaut syndrome

Salaam attacks

Symptomatic early myoclonic encephalopathy

West's syndrome

G40.40 Other generalized epilepsy and epileptic syndromes, not intractable

Other generalized epilepsy and epileptic syndromes without intractability

Other generalized epilepsy and epileptic syndromes NOS

G40.401 Other generalized epilepsy and epileptic syndromes, not intractable, with status epilepticus

G40.409 Other generalized epilepsy and epileptic syndromes, not intractable, without status epilepticus

G40.41 Other generalized epilepsy and epileptic syndromes, intractable

G40.411 Other generalized epilepsy and epileptic syndromes, intractable, with status epilepticus

G40.419 Other generalized epilepsy and epileptic syndromes, intractable, without status epilepticus

G40.5 Special epileptic syndromes

Epilepsia partialis continua [Kozhevnikof]

Epileptic seizures related to alcohol

Epileptic seizures related to drugs

Epileptic seizures related to hormonal changes

Epileptic seizures related to sleep deprivation

Epileptic seizures related to stress

G40.50 Special epileptic syndromes, not intractable

Special epileptic syndromes without intractability

G40.501 Special epileptic syndromes, not intractable, with status epilepticus

G40. 509 Special epileptic syndromes, not intractable, without status epilepticus

Special epileptic syndromes NOS

G40.51 Special epileptic syndromes, intractable

G40.511 Special epileptic syndromes, intractable, with status epilepticus

G40.519 Special epileptic syndromes, intractable, without status epilepticus

G40.8 Other epilepsy and seizures

Epilepsies and epileptic syndromes undetermined as to whether they are focal or generalized

G40.80 Other epilepsy, not intractable

Other epilepsy without intractability

G40.801 Other epilepsy, not intractable, with status epilepticus

G40.809 Other epilepsy, not intractable, without status epilepticus

Other epilepsy NOS

G40.81 Other epilepsy, intractable

G40.811 Other epilepsy, intractable, with status epilepticus

G40.819 Other epilepsy, intractable, without status epilepticus

G40.89 Other seizures

Excludes1: recurrent seizures NOS (G40.909)

seizure NOS (R56.9)

G40.9 Epilepsy, unspecified

G40.90 Epilepsy, unspecified, not intractable

Epilepsy, unspecified, without intractability

G40.901 Epilepsy, unspecified, not intractable, with status epilepticus

G40.909 Epilepsy, unspecified, not intractable, without status epilepticus

Epilepsy NOS

Epileptic convulsions NOS

Epileptic fits NOS

Epileptic seizures NOS

Recurrent seizures NOS

G40.91 Epilepsy, unspecified, intractable

Intractable seizure disorder NOS

G40.911 Epilepsy, unspecified, intractable, with status epilepticus

G40.919 Epilepsy, unspecified, intractable, without status epilepticus

G43 Migraine

Note: the following terms are to be considered equivalent to intractable: pharmacoresistant (pharmacologically resistant), treatment resistant, refractory (medically) and poorly controlled

Excludes1: headache NOS (R51)

headache syndromes (G44.-)

lower half migraine (G44.00)

G43.0 Migraine without aura

Common migraine

Excludes1: chronic migraine without aura (G43.7)

G43.00 Migraine without aura, not intractable

G43.001 Migraine without aura, not intractable, with status migrainosus

G43.009 Migraine without aura, not intractable, without status migrainosus

Migraine without aura NOS

G43.01 Migraine without aura, intractable

G43.011 Migraine without aura, intractable, with status migrainosus

G43.019 Migraine without aura, intractable, without status migrainosus

G43.1 Migraine with aura

Basilar migraine

Classical migraine

Migraine equivalents

Migraine preceded or accompanied by transient focal neurological phenomena

Migraine triggered seizures

Migraine with acute-onset aura

Migraine with aura without headache (migraine equivalents)

Migraine with prolonged aura

Migraine with typical aura

Retinal migraine

Code also any associated seizure (G40.-, R56.9)

Excludes1: persistent migraine aura (G43.5-, G43.6-)

G43.10 Migraine with aura, not intractable

G43.101 Migraine with aura, not intractable, with status migrainosus

G43.109 Migraine with aura, not intractable, without status migrainosus

Migraine with aura NOS

G43.11 Migraine with aura, intractable

G43.111 Migraine with aura, intractable, with status migrainosus

G43.119 Migraine with aura, intractable, without status migrainosus

G43. 4 Hemiplegic migraine

Familial migraine

Sporadic migraine

G43.40 Hemiplegic migraine, not intractable

G43.401 Hemiplegic migraine, not intractable, with status migrainosus

G43.409 Hemiplegic migraine, not intractable, without status migrainosus

Hemiplegic migraine NOS

G43.41 Hemiplegic migraine, intractable

G43.411 Hemiplegic migraine, intractable, with status migrainosus

G43.419 Hemiplegic migraine, intractable, without status migrainosus

G43.5 Persistent migraine aura without cerebral infarction

G43.50 Persistent migraine aura without cerebral infarction, not intractable

G43.501 Persistent migraine aura without cerebral infarction, not intractable, with status migrainosus

G43.509 Persistent migraine aura without cerebral infarction, not intractable, without status migrainosus

Persistent migraine aura NOS

G43.51 Persistent migraine aura without cerebral infarction, intractable

G43.511 Persistent migraine aura without cerebral infarction, intractable, with status migrainosus

G43.519 Persistent migraine aura without cerebral infarction, intractable, without status migrainosus

G43.6 Persistent migraine aura with cerebral infarction

Code also the type of cerebral infarction (I63.-)

G43.60 Persistent migraine aura with cerebral infarction, not intractable

G43.601 Persistent migraine aura with cerebral infarction, not intractable, with status migrainosus

G43.609 Persistent migraine aura with cerebral infarction, not intractable, without status migrainosus

G43.61 Persistent migraine aura with cerebral infarction, intractable

G43. 611 Persistent migraine aura with cerebral infarction, intractable, with status migrainosus

G43.619 Persistent migraine aura with cerebral infarction, intractable, without status migrainosus

G43.7 Chronic migraine without aura

Transformed migraine

Excludes1: migraine without aura (G43.0-)

G43.70 Chronic migraine without aura, not intractable

G43.701 Chronic migraine without aura, not intractable, with status migrainosus

G43.709 Chronic migraine without aura, not intractable, without status migrainosus

Chronic migraine without aura NOS

G43.71 Chronic migraine without aura, intractable

G43.711 Chronic migraine without aura, intractable, with status migrainosus

G43.719 Chronic migraine without aura, intractable, without status migrainosus

G43.a Cyclical vomiting

G43.a0 Cyclical vomiting, not intractable

G43.a01 Cyclical vomiting, not intractable, with status migrainosus

G43.a09 Cyclical vomiting, not intractable, without status migrainosus

Cyclical vomiting NOS

G43.a1 Cyclical vomiting, intractable

G43.a11 Cyclical vomiting, intractable, with status migrainosus

G43.a19 Cyclical vomiting, intractable, without status migrainosus

G43.b Ophthalmoplegic migraine

G43.b0 Ophthalmoplegic migraine, not intractable

G43.b01 Ophthalmoplegic migraine, not intractable, with status migrainosus

G43.b09 Ophthalmoplegic migraine, not intractable, without status migrainosus

Ophthalmoplegic migraine NOS

G43.b1 Ophthalmoplegic migraine, intractable

G43.b11 Ophthalmoplegic migraine, intractable, with status migrainosus

G43.b19 Ophthalmoplegic migraine, intractable, without status migrainosus

G43.c Periodic headache syndromes in child or adult

G43. c0 Periodic headache syndromes in child or adult, not intractable

G43.c01 Periodic headache syndromes in child or adult, not intractable, with status migrainosus

G43.c09 Periodic headache syndromes in child or adult, not intractable, without status migrainosus

Periodic headache syndromes in child or adult NOS

G43.c1 Periodic headache syndromes in child or adult, intractable

G43.c11 Periodic headache syndromes in child or adult, intractable, with status migrainosus

G43.c19 Periodic headache syndromes in child or adult, intractable, without status migrainosus

G43.d Menstrual migraine

Menstrual headache

Menstrually related migraine

Pre-menstrual headache

Pre-menstrual migraine

Pure menstrual migarine

Code also associated premenstrual tension syndrome (N94.3)

G43.d0 Menstrual migraine, not intractable

G43.d01 Menstrual migraine, not intractable, with status migrainosus

G43.d09 Menstrual migraine, not intractable, without status migrainosus

Menstrual migraine NOS

G43.d1 Menstrual migraine, intractable

G43.d11 Menstrual migraine, intractable, with status migrainosus

G43.d19 Menstrual migraine, intractable, without status migrainosus

G43.8 Other migraine

G43.80 Other migraine, not intractable

G43.801 Other migraine, not intractable, with status migrainosus

G43.809 Other migraine, not intractable, without status migrainosus

G43.81 Other migraine, intractable

G43.811 Other migraine, intractable, with status migrainosus

G43.819 Other migraine, intractable, without status migrainosus

G43.9 Migraine, unspecified

G43.90 Migraine, unspecified, not intractable

G43.901 Migraine, unspecified, not intractable, with status migrainosus

Status migrainosus NOS

G43.909 Migraine, unspecified, not intractable, without status migrainosus

Migraine NOS

G43.91 Migraine, unspecified, intractable

G43.911 Migraine, unspecified, not intractable, with status migrainosus

G43.919 Migraine, unspecified, not intractable, without status migrainosus

G44 Other headache syndromes

Excludes1: headache NOS (R51)

Excludes2: atypical facial pain (G50.1)

headache due to lumbar puncture (G97.1)

migraines (G43.-)

trigeminal neuralgia (G50.0)

G44.0 Cluster headaches and other trigeminal autonomic cephalgias (TAC)

G44.00 Cluster headache syndrome, unspecified

Ciliary neuralgia

Cluster headache NOS

Histamine cephalgia

Lower half migraine

Migrainous neuralgia

G44.001 Cluster headache syndrome, unspecified, intractable

G44.009 Cluster headache syndrome, unspecified, not intractable

Cluster headache syndrome NOS

G44.01 Episodic cluster headache

G44.011 Episodic cluster headache, intractable

G44.019 Episodic cluster headache, not intractable

Episodic cluster headache NOS

G44.02 Chronic cluster headache

G44.021 Chronic cluster headache, intractable

G44.029 Chronic cluster headache, not intractable

Chronic cluster headache NOS

G44.03 Episodic paroxysmal hemicrania

Paroxysmal hemicrania NOS

G44.031 Episodic paroxysmal hemicrania, intractable

G44.039 Episodic paroxysmal hemicrania, not intractable

Episodic paroxysmal hemicrania NOS

G44.04 Chronic paroxysmal hemicrania

G44.041 Chronic paroxysmal hemicrania, intractable

G44. 049 Chronic paroxysmal hemicrania, not intractable

Chronic paroxysmal hemicrania NOS

G44.05 Short lasting unilateral neuralgiform headache with conjunctival injection and tearing (SUNCT)

G44.051 Short lasting unilateral neuralgiform headache with conjunctival injection and tearing (SUNCT), intractable

G44.059 Short lasting unilateral neuralgiform headache with conjunctival injection and tearing (SUNCT), not intractable

Short lasting unilateral neuralgiform headache with conjunctival injection and tearing (SUNCT) NOS

G44.09 Other trigeminal autonomic cephalgias (TAC)

G44.091 Other trigeminal autonomic cephalgias (TAC), intractable

G44.099 Other trigeminal autonomic cephalgias (TAC), not intractable

G44.1 Vascular headache, not elsewhere classified

G44.10 Vascular headache, not elsewhere classified, not intractable

Vascular headache NOS

G44.11 Vascular headache, not elsewhere classified, intractable

G44.2 Tension-type headache

G44.20 Tension-type headache, unspecified

G44.201 Tension-type headache, unspecified, intractable

G44.209 Tension-type headache, unspecified, not intractable

Tension headache NOS

G44.21 Episodic tension-type headache

G44.211 Episodic tension-type headache, intractable

G44.219 Episodic tension-type headache, not intractable

Episodic tension-type headache NOS

G44.22 Chronic tension-type headache

G44.221 Chronic tension-type headache, intractable

G44.229 Chronic tension-type headache, not intractable

Chronic tension-type headache NOS

G44.3 Post-traumatic headache

Code first: postconcussional syndrome (F07.81)

G44.30 Post-traumatic headache, unspecified

G44.301 Post-traumatic headache, unspecified, intractable

G44. 309 Post-traumatic headache, unspecified, not intractable

Post-traumatic headache NOS

G44.31 Acute post-traumatic headache

G44.311 Acute post-traumatic headache, intractable

G44.319 Acute post-traumatic headache, not intractable

Acute post-traumatic headache NOS

G44.32 Chronic post-traumatic headache

G44.321 Chronic post-traumatic headache, intractable

G44.329 Chronic post-traumatic headache, not intractable

Chronic post-traumatic headache NOS

G44.4 Drug-induced headache, not elsewhere classified

Medication overuse headache

Code first (T36-T50) to identify drug

G44.40 Drug-induced headache, not elsewhere classified, not intractable

G44.41 Drug-induced headache, not elsewhere classified, intractable

G44.5 Complicated headache syndromes

G44.51 Hemicrania continua

G44.52 New daily persistent headache (NDPH)

G44.53 Primary thunderclap headache

G44.59 Other complicated headache syndrome

G44.8 Other specified headache syndromes

G44.81 Hypnic headache

G44.82 Headache associated with sexual activity

Orgasmic headache

Preorgasmic headache

G44.83 Primary cough headache

G44.84 Primary exertional headache

G44.85 Primary stabbing headache

G44.89 Other headache syndrome

G45 Transient cerebral ischemic attacks and related syndromes

Excludes1: neonatal cerebral ischemia (P91.0)

transient retinal artery occlusion (H34.0-)

G45.0 Vertebro-basilar artery syndrome

G45.1 Carotid artery syndrome (hemispheric)

G45.2 Multiple and bilateral precerebral artery syndromes

G45.3 Amaurosis fugax

G45.4 Transient global amnesia

Excludes1: amnesia NOS (R41.3)

G45.8 Other transient cerebral ischemic attacks and related syndromes

G45.9 Transient cerebral ischemic attack, unspecified

Spasm of cerebral artery

TIA

Transient cerebral ischemia NOS

G46 Vascular syndromes of brain in cerebrovascular diseases

Code first underlying cerebrovascular disease (I60-I69)

G46.0 Middle cerebral artery syndrome

G46.1 Anterior cerebral artery syndrome

G46.2 Posterior cerebral artery syndrome

G46.3 Brain stem stroke syndrome

Benedikt syndrome

Claude syndrome

Foville syndrome

Millard-Gubler syndrome

Wallenberg syndrome

Weber syndrome

G46.4 Cerebellar stroke syndrome

G46.5 Pure motor lacunar syndrome

G46.6 Pure sensory lacunar syndrome

G46.7 Other lacunar syndromes

G46.8 Other vascular syndromes of brain in cerebrovascular diseases

G47 Sleep disorders

Excludes2: nightmares (F51.5)

nonorganic sleep disorders (F51.-)

sleep terrors (F51.4)

sleepwalking (F51.3)

G47.0 Insomnia

Excludes2: alcohol related insomnia (F10.182, F10.282, F10.982)

drug related insomnia (F11.182, F11.282, F11.982, F13.182, F13.282, F13.982, F14.182, F14.282, F14.982, F15.182, F15.282, F15.982, F19.182, F19.282, F19.982)

idiopathic insomnia (F51.01)

insomnia due to a mental disorder (F51.05)

insomnia not due to a substance or known physiological condition (F51.0-)

nonorganic insomnia (F51.0-)

primary insomnia (F51.01)

sleep apnea (G47.3-)

G47.00 Insomnia, unspecified

Insomnia NOS

G47.01 Insomnia due to medical condition

Code also associated medical condition

G47.09 Other insomnia

G47.1 Hypersomnia

Excludes2: alcohol-related hypersomnia (F10.182, F10.282, F10.982)

drugrelated hypersomnia (F11.182, F11.282, F11.982, F13.182, F13.282, F13.982, F14.182, F14.282, F14.982, F15.182, F15.282, F15.982, F19.182, F19.282, F19.982)

hypersomnia due to a mental disorder (F51.13)

hypersomnia not due to a substance or known physiological condition (F51.11)

primary hypersomnia (F51.11)

sleep apnea (G47.3-)

G47.10 Hypersomnia, unspecified

Hypersomnia NOS

G47.11 Idiopathic hypersomnia with long sleep time

Idiopathic hypersomnia NOS

G47.12 Idiopathic hypersomnia without long sleep time

G47.13 Recurrent hypersomnia

Kleine-Levin syndrome

Menstrual related hypersomnia

G47.14 Hypersomnia due to medical condition

Code also associated medical condition

G47.19 Other hypersomnia

G47.2 Circadian rhythm sleep disorders

Disorders of the sleep wake schedule

Inversion of nyctohemeral rhythm

Inversion of sleep rhythm

G47.20 Circadian rhythm sleep disorder, unspecified type

Sleep wake schedule disorder NOS

G47.21 Circadian rhythm sleep disorder, delayed sleep phase type

Delayed sleep phase syndrome

G47.22 Circadian rhythm sleep disorder, advanced sleep phase type

G47.23 Circadian rhythm sleep disorder, irregular sleep wake type

Irregular sleep-wake pattern

G47.24 Circadian rhythm sleep disorder, free running type

G47.25 Circadian rhythm sleep disorder, jet lag type

G47.26 Circadian rhythm sleep disorder, shift work type

G47.27 Circadian rhythm sleep disorder in conditions classified elsewhere

Code first underlying condition

G47.29 Other circadian rhythm sleep disorder

G47.3 Sleep apnea

Code also any associated underlying condition

Excludes1: apnea NOS R06.81

Cheyne-Stokes breathing (R06.3)

pickwickian syndrome (E66.2)

sleep apnea of newborn (P28.3)

G47. 30 Sleep apnea, unspecified

Sleep apnea NOS

G47.31 Primary central sleep apnea

G47.32 High altitude periodic breathing

G47.33 Obstructive sleep apnea (adult) (pediatric)

G47.34 Idiopathic sleep related nonobstructive alveolar hypoventilation

Sleep related hypoxia

G47.35 Congenital central alveolar hypoventilation syndrome

G47.36 Sleep related hypoventilation in conditions classified elsewhere

Sleep related hypoxemia in conditions classified elsewhere

Code first underlying condition

G47.37 Central sleep apnea in conditions classified elsewhere

Code first underlying condition

G47.39 Other sleep apnea

G47.4 Narcolepsy and cataplexy

G47.41 Narcolepsy

G47.411 Narcolepsy with cataplexy

G47.419 Narcolepsy without cataplexy

Narcolepsy NOS

G47.42 Narcolepsy in conditions classified elsewhere

G47.421 Narcolepsy in conditions classified elsewhere with cataplexy

G47.429 Narcolepsy in conditions classified elsewhere without cataplexy

G47.5 Parasomnia

Excludes1: alcohol induced parasomnia (F10.182, F10.282, F10.982)

drug induced parasomnia (F11.182, F11.282, F11.982, F13.182, F13.282, F13.982, F14.182, F14.282, F14.982, F15.182, F15.282, F15.982, F19.182, F19.282, F19.982)

parasomnia not due to a substance or known physiological condition (F51.8)

G47.50 Parasomnia, unspecified

Parasomnia NOS

G47.51 Confusional arousals

G47.52 REM sleep behavior disorder

G47.53 Recurrent isolated sleep paralysis

G47.54 Parasomnia in conditions classified elsewhere

Code first underlying condition

G47.59 Other parasomnia

G47.6 Sleep related movement disorders

Excludes2: restless legs syndrome (G25.81)

G47.61 Periodic limb movement disorder

G47.62 Sleep related leg cramps

G47.63 Sleep related bruxism

Excludes1: psychogenic bruxism (F45.8)

G47.69 Other sleep related movement disorders

G47.8 Other sleep disorders

G47.9 Sleep disorder, unspecified

Sleep disorder NOS

Nerve, nerve root and plexus disorders (G50-G59)

Excludes1: current traumatic nerve, nerve root and plexus disorders - see Injury, nerve by body region

neuralgia NOS (M79.2)

neuritis NOS (M79.2)

peripheral neuritis in pregnancy (O26.82-)

radiculitis NOS (M54.1-)

G50 Disorders of trigeminal nerve

Includes disorders of 5th cranial nerve

G50.0 Trigeminal neuralgia

Syndrome of paroxysmal facial pain

Tic douloureux

G50.1 Atypical facial pain

G50.8 Other disorders of trigeminal nerve

G50.9 Disorder of trigeminal nerve, unspecified

G51 Facial nerve disorders

Includes disorders of 7th cranial nerve

G51.0 Bell's palsy

Facial palsy

G51.1 Geniculate ganglionitis

Excludes1: postherpetic geniculate ganglionitis (B02.21)

G51.2 Melkersson's syndrome

Melkersson-Rosenthal syndrome

G51.3 Clonic hemifacial spasm

G51.4 Facial myokymia

G51.8 Other disorders of facial nerve

G51.9 Disorder of facial nerve, unspecified

G52 Disorders of other cranial nerves

Excludes2: disorders of acoustic [8th] nerve (H93.3)

disorders of optic [2nd] nerve (H46, H47.0)

paralytic strabismus due to nerve palsy (H49.0-H49.2)

G52.0 Disorders of olfactory nerve

Disorders of 1st cranial nerve

G52.1 Disorders of glossopharyngeal nerve

Disorder of 9th cranial nerve

Glossopharyngeal neuralgia

G52.2 Disorders of vagus nerve

Disorders of pneumogastric [10th] nerve

G52.3 Disorders of hypoglossal nerve

Disorders of 12th cranial nerve

G52.7 Disorders of multiple cranial nerves

Polyneuritis cranialis

G52.8 Disorders of other specified cranial nerves

G52.9 Cranial nerve disorder, unspecified

G53 Cranial nerve disorders in diseases classified elsewhere

Code first underlying disease, such as:

neoplasm (C00-D48)

Excludes1: multiple cranial nerve palsy in sarcoidosis (D86.82)

multiple cranial nerve palsy in syphilis (A52.15)

postherpetic geniculate ganglionitis (B02.21)

postherpetic trigeminal neuralgia (B02.22)

G54 Nerve root and plexus disorders

Excludes1: current traumatic nerve root and plexus disorders - see nerve injury by body region

intervertebral disc disorders (M50-M51)

neuralgia or neuritis NOS (M79.2)

neuritis or radiculitis:

brachial NOS (M54.13)

lumbar NOS (M54.16)

lumbosacral NOS (M54.17)

thoracic NOS (M54.14)

radiculitis NOS (M54.10)

radiculopathy NOS (M54.10)

spondylosis (M47.-)

G54.0 Brachial plexus disorders

Thoracic outlet syndrome

G54.1 Lumbosacral plexus disorders

G54.2 Cervical root disorders, not elsewhere classified

G54.3 Thoracic root disorders, not elsewhere classified

G54.4 Lumbosacral root disorders, not elsewhere classified

G54.5 Neuralgic amyotrophy

Parsonage-Aldren-Turner syndrome

Shoulder-girdle neuritis

Excludes1: neuralgic amyotrophy in diabetes mellitus (E09-E13 with .44)

G54.6 Phantom limb syndrome with pain

G54.7 Phantom limb syndrome without pain

Phantom limb syndrome NOS

G54. 8 Other nerve root and plexus disorders

G54.9 Nerve root and plexus disorder, unspecified

G55 Nerve root and plexus compressions in diseases classified elsewhere

Code first underlying disease, such as:

neoplasm (C00-D48)

Excludes1: nerve root compression (due to) (in):

ankylosing spondylitis (M45.-)

dorsopathies (M53.-, M54.-)

intervertebral disc disorders (M50.1.-, M51.1.-)

spondylopathies (M46.-, M48.-)

spondylosis (M47.0-M47.2.-)

G56 Mononeuropathies of upper limb

Excludes1: current traumatic nerve disorder - see nerve injury by body region

G56.0 Carpal tunnel syndrome

G56.00 Carpal tunnel syndrome, unspecified side

G56.01 Carpal tunnel syndrome, right side

G56.02 Carpal tunnel syndrome, left side

G56.1 Other lesions of median nerve

G56.10 Other lesions of median nerve, unspecified side

G56.11 Other lesions of median nerve, right side

G56.12 Other lesions of median nerve, left side

G56.2 Lesion of ulnar nerve

Tardy ulnar nerve palsy

G56.20 Lesion of ulnar nerve, unspecified side

G56.21 Lesion of ulnar nerve, right side

G56.22 Lesion of ulnar nerve, left side

G56.3 Lesion of radial nerve

G56.30 Lesion of radial nerve, unspecified side

G56.31 Lesion of radial nerve, right side

G56.32 Lesion of radial nerve, left side

G56.4 Causalgia of upper limb

Complex regional pain syndrome II of upper limb

Excludes1: complex regional pain syndrome I of lower limb (G90.52-)

complex regional pain syndrome I of upper limb (G90.51-)

complex regional pain syndrome II of lower limb (G57.7-)

reflex sympathetic dystrophy of lower limb (G90.52-)

reflex sympathetic dystrophy of upper limb (G90.51-)

G56.40 Causalgia of upper limb, unspecified side

G56.41 Causalgia of upper limb, right side

G56.42 Causalgia of upper limb, left side

G56.8 Other mononeuropathies of upper limb

Interdigital neuroma of upper limb

G56.80 Other mononeuropathies of upper limb, unspecified side

G56. 81 Other mononeuropathies of upper limb, right side

G56.82 Other mononeuropathies of upper limb, left side

G56.9 Mononeuropathy of upper limb, unspecified

G56.90 Mononeuropathy of upper limb, unspecified, unspecified side

G56.91 Mononeuropathy of upper limb, unspecified, right side

G56.92 Mononeuropathy of upper limb, unspecified, left side

G57 Mononeuropathies of lower limb

Excludes1: current traumatic nerve disorder - see nerve injury by body region

G57.0 Lesion of sciatic nerve

Excludes1: sciatica NOS (M54.3-)

Excludes2: sciatica attributed to intervertebral disc disorder (M51.1.-)

G57.00 Lesion of sciatic nerve, unspecified side

G57.01 Lesion of sciatic nerve, right side

G57.02 Lesion of sciatic nerve, left side

G57.1 Meralgia paresthetica

Lateral cutaneous nerve of thigh syndrome

G57.10 Meralgia paresthetica, unspecified side

G57.11 Meralgia paresthetica, right side

G57.12 Meralgia paresthetica, left side

G57.2 Lesion of femoral nerve

G57.20 Lesion of femoral nerve, unspecified side

G57.21 Lesion of femoral nerve, right side

G57.22 Lesion of femoral nerve, left side

G57.3 Lesion of lateral popliteal nerve

Peroneal nerve palsy

G57.30 Lesion of lateral popliteal nerve, unspecified side

G57.31 Lesion of lateral popliteal nerve, right side

G57.32 Lesion of lateral popliteal nerve, left side

G57.4 Lesion of medial popliteal nerve

G57.40 Lesion of medial popliteal nerve, unspecified side

G57.41 Lesion of medial popliteal nerve, right side

G57.42 Lesion of medial popliteal nerve, left side

G57.5 Tarsal tunnel syndrome

G57.50 Tarsal tunnel syndrome, unspecified side

G57.51 Tarsal tunnel syndrome, right side

G57.52 Tarsal tunnel syndrome, left side

G57.6 Lesion of plantar nerve

Morton's metatarsalgia

G57.60 Lesion of plantar nerve, unspecified side

G57.61 Lesion of plantar nerve, right side

G57.62 Lesion of plantar nerve, left side

G57.7 Causalgia of lower limb

Complex regional pain syndrome II of lower limb

Excludes1: complex regional pain syndrome I of lower limb (G90.52-)

complex regional pain syndrome I of upper limb (G90.51-)

complex regional pain syndrome II of upper limb (G56.4-)

reflex sympathetic dystrophy of lower limb (G90.52-)

reflex sympathetic dystrophy of upper limb (G90.51-)

G57.70 Causalgia of lower limb, unspecified side

G57.71 Causalgia of lower limb, right side

G57.72 Causalgia of lower limb, left side

G57.8 Other mononeuropathies of lower limb

Interdigital neuroma of lower limb

G57.80 Other mononeuropathies of lower limb, unspecified side

G57.81 Other mononeuropathies of lower limb, right side

G57.82 Other mononeuropathies of lower limb, left side

G57.9 Mononeuropathy of lower limb, unspecified

G57.90 Mononeuropathy of lower limb, unspecified, unspecified side

G57.91 Mononeuropathy of lower limb, unspecified, right side

G57.92 Mononeuropathy of lower limb, unspecified, left side

G58 Other mononeuropathies

G58.0 Intercostal neuropathy

G58.7 Mononeuritis multiplex

G58.8 Other specified mononeuropathies

G58.9 Mononeuropathy, unspecified

G59 Mononeuropathy in diseases classified elsewhere

Code first underlying disease

Excludes1: diabetic mononeuropathy (E09-E14 with .41)

syphilitic nerve paralysis (A52.19)

syphilitic neuritis (A52.15)

tuberculous mononeuropathy (A17.83)

Polyneuropathies and other disorders of the peripheral nervous system (G60-G64)

Excludes1: neuralgia NOS (M79.2)

neuritis NOS (M79.2)

peripheral neuritis in pregnancy (O26.82-)

radiculitis NOS (M54.10)

G60 Hereditary and idiopathic neuropathy

G60.0 Hereditary motor and sensory neuropathy

Charcot-Marie-Tooth disease

Déjérine-Sottas disease

Hereditary motor and sensory neuropathy, types I-IV

Hypertrophic neuropathy of infancy

Peroneal muscular atrophy (axonal type) (hypertrophic type)

RoussyLevy syndrome

G60.1 Refsum's disease

Infantile Refsum disease

G60.2 Neuropathy in association with hereditary ataxia

G60.3 Idiopathic progressive neuropathy

G60.8 Other hereditary and idiopathic neuropathies

Dominantly inherited sensory neuropathy

Morvan's disease

Nelaton's syndrome

Recessively inherited sensory neuropathy

G60.9 Hereditary and idiopathic neuropathy, unspecified

G61 Inflammatory polyneuropathy

G61.0 Guillain-Barre syndrome

Acute (post-)infective polyneuritis

Miller Fisher Syndrome

G61.1 Serum neuropathy

Code first (T50.9-) to identify serum

G61.8 Other inflammatory polyneuropathies

G61.81 Chronic inflammatory demyelinating polyneuritis

G61.89 Other inflammatory polyneuropathies

G61.9 Inflammatory polyneuropathy, unspecified

G62 Other and unspecified polyneuropathies

G62.0 Drug-induced polyneuropathy

Code first (T36-T50) to identify drug

G62.1 Alcoholic polyneuropathy

G62.2 Polyneuropathy due to other toxic agents

Code first (T51-T65) to identify toxic agent.

G62.8 Other specified polyneuropathies

G62.81 Critical illness polyneuropathy

Acute motor neuropathy

G62.82 Radiation-induced polyneuropathy

Use additional external cause code (W88-W90, X39.0-) to identify cause

G62.89 Other specified polyneuropathies

G62.9 Polyneuropathy, unspecified

Neuropathy NOS

G63 Polyneuropathy in diseases classified elsewhere

Code first underlying disease, such as:

amyloidosis (E85.-)

endocrine disease, except diabetes (E00-E07, E15-E16, E20-E34)

metabolic diseases (E70-E89)

neoplasm (C00-D48)

nutritional deficiency (E40-E64)

Excludes1: polyneuropathy (in):

diabetes mellitus (E09-E13 with .42)

diphtheria (A36.83)

infectious mononucleosis (B27.0-B27.9 with 1)

Lyme disease (A69.22)

mumps (B26.84)

postherpetic (B02.23)

rheumatoid arthritis (M05.33)

scleroderma (M34.83)

systemic lupus erythematosus (M32.19)

G64 Other disorders of peripheral nervous system

Disorder of peripheral nervous system NOS

G65 Sequelae of inflammatory and toxic polyneuropathies

Code first condition resulting from (sequela) of inflammatory and toxic polyneuropathies

G65.0 Sequelae of Guillain-Barr? syndrome

G65.1 Sequelae of other inflammatory polyneuropathy

G65.2 Sequelae of toxic polyneuropathy

Diseases of myoneural junction and muscle (G70-G73)

G70 Myasthenia gravis and other myoneural disorders

Excludes1: botulism (A05.1, A48.51- A48.52)

transient neonatal myasthenia gravis (P94.0)

G70.0 Myasthenia gravis

G70.00 Myasthenia gravis without (acute) exacerbation

Myasthenia gravis NOS

G70.01 Myasthenia gravis with (acute) exacerbation

Myasthenia gravis in crisis

G70.1 Toxic myoneural disorders

Code first (T51-T65) to identify toxic agent.

G70.2 Congenital and developmental myasthenia

G70.8 Other specified myoneural disorders

G70.9 Myoneural disorder, unspecified

G71 Primary disorders of muscles

Excludes2: arthrogryposis multiplex congenita (Q74.3)

metabolic disorders (E70-E90)

myositis (M60.-)

G71.0 Muscular dystrophy

Autosomal recessive, childhood type, muscular dystrophy resembling Duchenne or Becker muscular dystrophy

Benign [Becker] muscular dystrophy

Benign scapuloperoneal muscular dystrophy with early contractures [Emery-Dreifuss]

Distal muscular dystrophy

Facioscapulohumeral muscular dystrophy

Limb-girdle muscular dystrophy

Ocular muscular dystrophy

Oculopharyngeal muscular dystrophy

Scapuloperoneal muscular dystrophy

Severe [Duchenne] muscular dystrophy

Excludes1: congenital muscular dystrophy NOS (G71.2)

congenital muscular dystrophy with specific morphological abnormalities of the muscle fiber (G71.2)

G71.1 Myotonic disorders

G71.11 Myotonic muscular dystrophy

Dystrophia myotonica [Steinert]

Myotonia atrophica

Myotonic dystrophy

Proximal myotonic myopathy (PROMM)

Steinert disease

G71.12 Myotonia congenita

Acetazolamide responsive myotonia congenita

Dominant myotonia congenita [Thomsen disease]

Myotonia levior

Recessive myotonia congenita [Becker disease]

G71.13 Myotonic chondrodystrophy

Chondrodystrophic myotonia

Congenital myotonic chondrodystrophy

Schwartz-Jampel disease

G71.14 Drug induced myotonia

Code first (T36-T50) to identify drug

G71.19 Other specified myotonic disorders

Myotonia fluctuans

Myotonia permanens

Neuromyotonia [Isaacs]

Paramyotonia congenita (of von Eulenburg)

Pseudomyotonia

Symptomatic myotonia

G71.2 Congenital myopathies

Central core disease

Congenital muscular dystrophy NOS

Congenital muscular dystrophy with specific morphological abnormalities of the muscle fiber

Fiber-type disproportion

Minicore disease

Multicore disease

Myotubular (centronuclear) myopathy

Nemaline myopathy

Excludes1: arthrogryposis multiplex congenita (Q74.3)

G71. 3 Mitochondrial myopathy, not elsewhere classified

Excludes1: Kearns-Sayre syndrome (H49.81)

Leber's disease (H47.21)

Leigh's encephalopathy (G31.82)

mitochondrial metabolism disorders (E88.4.-)

Reye's syndrome (G93.7)

G71.8 Other primary disorders of muscles

G71.9 Primary disorder of muscle, unspecified

Hereditary myopathy NOS

G72 Other and unspecified myopathies

Excludes1: arthrogryposis multiplex congenita (Q74.3)

dermatopolymyositis (M33.-)

ischemic infarction of muscle (M62.2-)

myositis (M60.-)

polymyositis (M33.2.-)

G72.0 Drug-induced myopathy

Code first (T36-T50) to identify drug

G72.1 Alcoholic myopathy

Use additional code to identify alcoholism (F10.-)

G72.2 Myopathy due to other toxic agents

Code first (T51-T65) to identify toxic agent.

G72.3 Periodic paralysis

Familial periodic paralysis

Hyperkalemic periodic paralysis (familial)

Hypokalemic periodic paralysis (familial)

Myotonic periodic paralysis (familial)

Normokalemic paralysis (familial)

Potassium sensitive periodic paralysis

Excludes1: paramyotonia congenita (of von Eulenburg) (G71.19)

G72.4 Inflammatory and immune myopathies, not elsewhere classified

G72.41 Inclusion body myositis [IBM]

G72.49 Other inflammatory and immune myopathies, not elsewhere classified

Inflammatory myopathy NOS

G72.8 Other specified myopathies

G72.81 Critical illness myopathy

Acute necrotizing myopathy

Acute quadriplegic myopathy

Intensive care (ICU) myopathy

Myopathy of critical illness

G72.89 Other specified myopathies

G72.9 Myopathy, unspecified

G73 Disorders of myoneural junction and muscle in diseases classified elsewhere

G73. 1 Lambert-Eaton syndrome

Code first underlying disease, such as:

malignant neoplasm of lung (C34.-)

other neoplastic disease (C00-D48)

Excludes1: Lambert-Eaton syndrome not associated with neoplasm (G70.8)

G73.3 Myasthenic syndromes in other diseases classified elsewhere

Code first underlying disease, such as:

neoplasm (C00-D498)

thyrotoxicosis (E05.-)

G73.7 Myopathy in diseases classified elsewhere

Code first underlying disease, such as:

hyperparathyroidism (E21.0, E21.3)

hypoparathyroidism (E20.-)

glycogen storage disease (E74.0)

lipid storage disorders (E75.-)

Excludes1: myopathy in:

rheumatoid arthritis (M05.32)

sarcoidosis (D86.87)

scleroderma (M34.82)

sicca syndrome [Sj?gren] (M35.03)

systemic lupus erythematosus (M32.19)

Cerebral palsy and other paralytic syndromes (G80-G83)

G80 Cerebral palsy

Excludes1: hereditary spastic paraplegia (G11.4)

G80.0 Spastic quadriplegic cerebral palsy

Congenital spastic paralysis (cerebral)

G80.1 Spastic diplegic cerebral palsy

Spastic cerebral palsy NOS

G80.2 Spastic hemiplegic cerebral palsy

G80.3 Athetoid cerebral palsy

Double athetosis (syndrome)

Dyskinetic cerebral palsy

Dystonic cerebral palsy

Vogt disease

G80.4 Ataxic cerebral palsy

G80.8 Other cerebral palsy

Mixed cerebral palsy syndromes

G80.9 Cerebral palsy, unspecified

Cerebral palsy NOS

G81 Hemiplegia and hemiparesis

Note: This category is to be used only when hemiplegia (complete)(incomplete) is reported without further specification, or is stated to be old or

longstanding but of unspecified cause. The category is also for use in multiple coding to identify these types of hemiplegia resulting from any cause.

Excludes1: congenital cerebral palsy (G80.-)

hemiplegia and hemiparesis due to sequela of cerebrovascular disease (I69.05-, I69.15-, I69.25-, I69.35-, I69.45-, I69.85-, I69.95-)

G81.0 Flaccid hemiplegia

G81.00 Flaccid hemiplegia affecting unspecified side

G81.01 Flaccid hemiplegia affecting right dominant side

G81.02 Flaccid hemiplegia affecting left dominant side

G81.03 Flaccid hemiplegia affecting right nondominant side

G81.04 Flaccid hemiplegia affecting left nondominant side

G81.1 Spastic hemiplegia

G81.10 Spastic hemiplegia affecting unspecified side

G81.11 Spastic hemiplegia affecting right dominant side

G81.12 Spastic hemiplegia affecting left dominant side

G81.13 Spastic hemiplegia affecting right nondominant side

G81.14 Spastic hemiplegia affecting left nondominant side

G81.9 Hemiplegia, unspecified

G81.90 Hemiplegia, unspecified affecting unspecified side

G81.91 Hemiplegia, unspecified affecting right dominant side

G81.92 Hemiplegia, unspecified affecting left dominant side

G81.93 Hemiplegia, unspecified affecting right nondominant side

G81.94 Hemiplegia, unspecified affecting left nondominant side

G82 Paraplegia (paraparesis) and quadriplegia (quadriparesis)

Note: This category is to be used only when the listed conditions are reported without further specification, or are stated to be old or longstanding but of unspecified cause. The category is also for use in multiple coding to identify these conditions resulting from any cause

Excludes1: congenital cerebral palsy (G80.-)

functional quadriplegia (R53.2)

hysterical paralysis (F44.4)

G82.2 Paraplegia

Paralysis of both lower limbs NOS

Paraparesis (lower) NOS

Paraplegia (lower) NOS

G82.20 Paraplegia, unspecified

G82.21 Paraplegia, complete

G82.22 Paraplegia, incomplete

G82.5 Quadriplegia

G82.50 Quadriplegia, unspecified

G82.51 Quadriplegia, C1-C4 complete

G82.52 Quadriplegia, C1-C4 incomplete

G82.53 Quadriplegia, C5-C7 complete

G82. 54 Quadriplegia, C5-C7 incomplete

G83 Other paralytic syndromes

Note: This category is to be used only when the listed conditions are reported without further specification, or are stated to be old or longstanding but of unspecified cause. The category is also for use in multiple coding to identify these conditions resulting from any cause.

Includes paralysis (complete) (incomplete), except as in G80-G82

G83.0 Diplegia of upper limbs

Diplegia (upper)

Paralysis of both upper limbs

G83.1 Monoplegia of lower limb

Paralysis of lower limb

Excludes1: monoplegia of lower limbs due to sequela of cerebrovascular disease (I69.04-, I69.14-, I69.24-, I69.34-, I69.44-, I69.84-, I69.94-)

G83.10 Monoplegia of lower limb affecting unspecified side

G83.11 Monoplegia of lower limb affecting right dominant side

G83.12 Monoplegia of lower limb affecting left dominant side

G83.13 Monoplegia of lower limb affecting right nondominant side

G83.14 Monoplegia of lower limb affecting left nondominant side

G83.2 Monoplegia of upper limb

Paralysis of upper limb

Excludes1: monoplegia of upper limbs due to sequela of cerebrovascular disease (I69.03-, I69.13-, I69.23-, I69.33-, I69.43-, I69.83-, I69.93-)

G83.20 Monoplegia of upper limb affecting unspecified side

G83.21 Monoplegia of upper limb affecting right dominant side

G83.22 Monoplegia of upper limb affecting left dominant side

G83.23 Monoplegia of upper limb affecting right nondominant side

G83.24 Monoplegia of upper limb affecting left nondominant side

G83.3 Monoplegia, unspecified

G83.30 Monoplegia, unspecified affecting unspecified side

G83.31 Monoplegia, unspecified affecting right dominant side

G83.32 Monoplegia, unspecified affecting left dominant side

G83.33 Monoplegia, unspecified affecting right nondominant side

G83.34 Monoplegia, unspecified affecting left nondominant side

G83.4 Cauda equina syndrome

Neurogenic bladder due to cauda equina syndrome

Excludes1: cord bladder NOS (G95.8)

neurogenic bladder NOS (N31.9)

G83. 5 Locked-in state

G83.8 Other specified paralytic syndromes

Excludes1: paralytic syndromes due to current spinal cord injury-code to spinal cord injury (S14, S24, S34)

G83.81 Brown-Sequard syndrome

G83.82 Anterior cord syndrome

G83.83 Posterior cord syndrome

G83.84 Todd's paralysis (postepileptic)

G83.89 Other specified paralytic syndromes

G83.9 Paralytic syndrome, unspecified

Other disorders of the nervous system (G89-G99)

G89 Pain, not elsewhere classified

Code also related psychological factors associated with pain (F45.42)

Excludes1: generalized pain NOS (R52)

pain disorders exclusively related to psychological factors (F45.41)

pain NOS (R52)

Excludes2: atypical face pain (G50.1)

headache syndromes (G44.-)

localized pain, unspecified type - code to pain by site, such as:

abdomen pain (R10.-)

back pain (M54.9)

breast pain (N64.4)

chest pain (R07.1-R07.9)

ear pain (H92.0-)

eye pain (H57.1)

headache (R51)

joint pain (M25.5-)

limb pain (M79.6-)

lumbar region pain (M54.57)

painful urination (R30.9)

pelvic and perineal pain (R10.2)

shoulder pain (M25.51-)

spine pain (M54.-)

throat pain (R07.0)

tongue pain (K14.6)

tooth pain (K08.8)

renal colic (N23)

migraines (G43.-)

myalgia (M79.1)

pain from prosthetic devices, implants, and grafts (T82.84, T83.84, T84.84, T85.84)

phantom limb syndrome with pain (G54.6)

vulvar vestibulitis (N94.810)

vulvodynia (N94.81-)

G89.0 Central pain syndrome

Déjérine-Roussy syndrome

Myelopathic pain syndrome

Thalamic pain syndrome (hyperesthetic)

G89.1 Acute pain, not elsewhere classified

G89.11 Acute pain due to trauma

G89.12 Acute post-thoracotomy pain

Post-thoracotomy pain NOS

G89.18 Other acute postprocedural pain

Postoperative pain NOS

Postprocedural pain NOS

G89.2 Chronic pain, not elsewhere classified

Excludes1: causalgia, lower limb (G57.7-)

causalgia, upper limb (G56.4-)

central pain syndrome (G89.0)

chronic pain syndrome (G89.4)

complex regional pain syndrome II, lower limb (G57.7-)

complex regional pain syndrome II, upper limb (G56.4-)

neoplasm related chronic pain (G89.3)

reflex sympathetic dystrophy (G90.5-)

G89.21 Chronic pain due to trauma

G89.22 Chronic post-thoracotomy pain

G89.28 Other chronic postprocedural pain

Other chronic postoperative pain

G89.3 Neoplasm related pain (acute) (chronic)

Cancer associated pain

Pain due to malignancy (primary) (secondary)

Tumor associated pain

G89.4 Chronic pain syndrome

Chronic pain associated with significant psychosocial dysfunction

G90 Disorders of autonomic nervous system

Excludes1: dysfunction of the autonomic nervous system due to alcohol (G31.2)

G90.0 Idiopathic peripheral autonomic neuropathy

G90.01 Carotid sinus syncope

Carotid sinus syndrome

G90.09 Other idiopathic peripheral autonomic neuropathy

Idiopathic peripheral autonomic neuropathy NOS

G90.1 Familial dysautonomia [Riley-Day]

G90.2 Horner's syndrome

Bernard(-Horner) syndrome

Cervical sympathetic dystrophy or paralysis

G90.3 Multi-system degeneration of the autonomic nervous system

Neurogenic orthostatic hypotension [Shy-Drager]

Excludes1: orthostatic hypotension NOS (I95.1)

G90.4 Autonomic dysreflexia

Use additional code to identify the cause, such as:

pressure ulcer (pressure area) (L89.-)

fecal impaction (K56.4)

urinary tract infection (N39.0)

G90.5 Complex regional pain syndrome I (CRPS I)

Reflex sympathetic dystrophy

Excludes1: causalgia of lower limb (G57.7-)

causalgia of upper limb (G56.4-)

complex regional pain syndrome II of lower limb (G57.7-)

complex regional pain syndrome II of upper limb (G56.4-)

G90.50 Complex regional pain syndrome I, unspecified

G90.51 Complex regional pain syndrome I of upper limb

G90.511 Complex regional pain syndrome I of right upper limb

G90.512 Complex regional pain syndrome I of left upper limb

G90.513 Complex regional pain syndrome I of upper limb, bilateral

G90.519 Complex regional pain syndrome I of unspecified upper limb

G90.52 Complex regional pain syndrome I of lower limb

G90.521 Complex regional pain syndrome I of right lower limb

G90.522 Complex regional pain syndrome I of left lower limb

G90.523 Complex regional pain syndrome I of lower limb, bilateral

G90.529 Complex regional pain syndrome I of unspecified lower limb

G90.59 Complex regional pain syndrome I of other specified site

G90.8 Other disorders of autonomic nervous system

G90.9 Disorder of the autonomic nervous system, unspecified

G91 Hydrocephalus

Includes acquired hydrocephalus

Excludes1: Arnold-Chiari syndrome with hydrocephalus (Q07.-)

congenital hydrocephalus (Q03.-)

spina bifida with hydrocephalus (Q05.-)

G91.0 Communicating hydrocephalus

Secondary normal pressure hydrocephalus

G91.1 Obstructive hydrocephalus

G91.2 (Idiopathic) normal pressure hydrocephalus

Normal pressure hydrocephalus NOS

G91.3 Post-traumatic hydrocephalus, unspecified

G91.4 Hydrocephalus in diseases classified elsewhere

Code first underlying condition, such as:

congenital syphilis (A50.4-)

neoplasm (C00-D48)

Excludes1: hydrocephalus due to congenital toxoplasmosis (P37.1)

G91.8 Other hydrocephalus

G91.9 Hydrocephalus, unspecified

G92 Toxic encephalopathy

Toxic encephalitis

Toxic metabolic encephalopathy

Code first (T51-T65) to identify toxic agent.

G93 Other disorders of brain

G93.0 Cerebral cysts

Arachnoid cyst

Porencephalic cyst, acquired

Excludes1: acquired periventricular cysts of newborn (P91.1)

congenital cerebral cysts (Q04.6)

G93.1 Anoxic brain damage, not elsewhere classified

Excludes1: cerebral anoxia due to anesthesia during labor and delivery (O74.3)

cerebral anoxia due to anesthesia during the puerperium (O89.2)

neonatal anoxia (P28.9)

G93.2 Benign intracranial hypertension

Excludes1: hypertensive encephalopathy (I67.4)

G93.3 Postviral fatigue syndrome

Benign myalgic encephalomyelitis

Excludes1: chronic fatigue syndrome NOS (R53.82)

G93.4 Other and unspecified encephalopathy

Excludes1: alcoholic encephalopathy (G31.2)

hypertensive encephalopathy (I67.4)

toxic (metabolic) encephalopathy (G92)

G93.40 Encephalopathy, unspecified

G93.41 Metabolic encephalopathy

Septic encephalopathy

G93.49 Other encephalopathy

Encephalopathy NEC

G93.5 Compression of brain

Arnold-Chiari type 1 compression of brain

Compression of brain (stem)

Herniation of brain (stem)

Excludes1: diffuse traumatic compression of brain (S06.2-)

focal traumatic compression of brain (S06.3-)

G93.6 Cerebral edema

Excludes1: cerebral edema due to birth injury (P11.0)

traumatic cerebral edema (S06.1-)

G93.7 Reye's syndrome

Code first (T39.0-), if salicylates-induced

G93.8 Other specified disorders of brain

G93.81 Temporal sclerosis

Hippocampal sclerosis

Mesial temporal sclerosis

G93.89 Other specified disorders of brain

Postradiation encephalopathy

G93.9 Disorder of brain, unspecified

G94 Other disorders of brain in diseases classified elsewhere

Code first underlying disease

Excludes1: encephalopathy in congenital syphilis (A50.49)

encephalopathy in influenza (J10.89)

encephalopathy in syphilis (A52.19)

hydrocephalus in diseases classified elsewhere (G91.4)

G95 Other and unspecified diseases of spinal cord

Excludes2: myelitis (G04.-)

G95.0 Syringomyelia and syringobulbia

G95.1 Vascular myelopathies

Excludes2: intraspinal phlebitis and thrombophlebitis, except non-pyogenic (G08)

G95.11 Acute infarction of spinal cord (embolic) (nonembolic)

Anoxia of spinal cord

Arterial thrombosis of spinal cord

G95.19 Other vascular myelopathies

Edema of spinal cord

Hematomyelia

Nonpyogenic intraspinal phlebitis and thrombophlebitis

Subacute necrotic myelopathy

G95.2 Other and unspecified cord compression

G95.20 Unspecified cord compression

G95.29 Other cord compression

G95.8 Other specified diseases of spinal cord

Excludes1: neurogenic bladder NOS (N31.9)

neurogenic bladder due to cauda equina syndrome (G83.4)

neuromuscular dysfunction of bladder without spinal cord lesion (N31.-)

G95.81 Conus medullaris syndrome

G95.89 Other specified diseases of spinal cord

Cord bladder NOS

Drug-induced myelopathy

Radiation-induced myelopathy

Excludes1: myelopathy NOS (G95.9)

G95.9 Disease of spinal cord, unspecified

Myelopathy NOS

G96 Other disorders of central nervous system

G96.0 Cerebrospinal fluid leak

Excludes1: cerebrospinal fluid leak from spinal puncture (G97.0)

G96.1 Disorders of meninges, not elsewhere classified

G96.11 Dural tear

Excludes1: accidental puncture or laceration of dura during a procedure (G97.41)

G96.12 Meningeal adhesions (cerebral) (spinal)

G96.19 Other disorders of meninges, not elsewhere classified

G96.8 Other specified disorders of central nervous system

G96.9 Disorder of central nervous system, unspecified

G97 Intraoperative and postprocedural complications and disorders of nervous system, not elsewhere classified

Excludes2: intraoperative and postprocedural cerebrovascular infarction (I97.81-, I97.82- )

G97.0 Cerebrospinal fluid leak from spinal puncture

G97.1 Other reaction to spinal and lumbar puncture

Headache due to lumbar puncture

G97.2 Intracranial hypotension following ventricular shunting

G97.3 Intraoperative hemorrhage and hematoma of a nervous system organ or structure complicating a procedure

Excludes1: intraoperative hemorrhage and hematoma of a nervous system organ or structure due to accidental puncture and laceration during a procedure (G97.4-)

G97.31 Intraoperative hemorrhage and hematoma of a nervous system organ or structure complicating a nervous system procedure

G97.32 Intraoperative hemorrhage and hematoma of a nervous system organ or structure complicating other procedure

G97.4 Accidental puncture and laceration of a nervous system organ or structure during a procedure

G97.41 Accidental puncture or laceration of dura during a procedure

Incidental (inadvertent) durotomy

G97.48 Accidental puncture and laceration of other nervous system organ or structure during a nervous system procedure

G97. 49 Accidental puncture and laceration of other nervous system organ or structure during other procedure

G97.5 Postprocedural hemorrhage and hematoma of a nervous system organ or structure following a procedure

G97.51 Postprocedural hemorrhage and hematoma of a nervous system organ or structure following a nervous system procedure

G97.52 Postprocedural hemorrhage and hematoma of a nervous system organ or structure following other procedure

G97.8 Other intraoperative and postprocedural complications and disorders of nervous system

Use additional code to further specify disorder

G97.81 Other intraoperative complications of nervous system

G97.82 Other postprocedural complications and disorders of nervous system

G98 Other disorders of nervous system not elsewhere classified

Includes nervous system disorder NOS

G98.0 Neurogenic arthritis, not elsewhere classified

Nonsyphilitic neurogenic arthropathy NEC

Nonsyphilitic neurogenic spondylopathy NEC

Excludes1: spondylopathy (in):

syringomyelia and syringobulbia (G95.0)

tabes dorsalis (A52.11)

G98.8 Other disorders of nervous system

Nervous system disorder NOS

G99 Other disorders of nervous system in diseases classified elsewhere

G99.0 Autonomic neuropathy in diseases classified elsewhere

Code first underlying disease, such as:

amyloidosis (E85.-)

gout ( M1a-, M10.-)

hyperthyroidism (E05.-)

Excludes1: diabetic autonomic neuropathy (E09-14 with .43)

G99.2 Myelopathy in diseases classified elsewhere

Code first underlying disease, such as:

neoplasm (C00-D48)

Excludes1: myelopathy in:

intervertebral disease (M50.0-, M51.0-)

spondylosis (M47.0-, M47.1-)

G99.8 Other specified disorders of nervous system in diseases classified elsewhere

Code first underlying disorder, such as:

amyloidosis (E85.-)

avitaminosis (E56.9)

Excludes1: nervous system involvement in:

cysticercosis (B69.0)

rubella (B06.0-)

syphilis (A52.1-)