Page:ICD-10-CM (2010).djvu/1135

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3 Congenital bullous ichthyosiform erythroderma

Q80.4 Harlequin fetus
Q80.8 Other congenital ichthyosis
Q80.9 Congenital ichthyosis, unspecified

Q81 Epidermolysis bullosa

Q81.0 Epidermolysis bullosa simplex
Excludes1: Cockayne's syndrome (Q87.1)
Q81.1 Epidermolysis bullosa letalis
Herlitz' syndrome
Q81.2 Epidermolysis bullosa dystrophica
Q81.8 Other epidermolysis bullosa
Q81.9 Epidermolysis bullosa, unspecified

Q82 Other congenital malformations of skin

Excludes1: acrodermatitis enteropathica (E83.2)
congenital erythropoietic porphyria (E80.0)
pilonidal cyst or sinus (L05.-)
Sturge-Weber (-Dimitri) syndrome (Q85.8)
Q82.0 Hereditary lymphedema
Q82.1 Xeroderma pigmentosum
Q82.2 Mastocytosis
Urticaria pigmentosa
Excludes1: malignant mastocytosis (C96.2)
Q82.3 Incontinentia pigmenti
Q82.4 Ectodermal dysplasia (anhidrotic)
Excludes1: Ellis-van Creveld syndrome (Q77.6)
Q82.5 Congenital non-neoplastic nevus
Birthmark NOS
Flammeus Nevus
Portwine Nevus
Sanguineous Nevus
Strawberry Nevus
Vascular Nevus NOS
Verrucous Nevus
Excludes2: caf? au lait spots (L81.3)
lentigo (L81.4)
nevus NOS (D22.-)
araneus nevus (I78.1)
melanocytic nevus (D22.-)
pigmented nevus (D22.-)
spider nevus (I78.1)
stellar nevus (I78.1)
Q82.8 Other specified congenital malformations of skin
Abnormal palmar creases
Accessory skin tags
Benign familial pemphigus [Hailey-Hailey]
Congenital