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0 Congenital absence and malformations of spleen
- Excludes1: isomerism of atrial appendages (with asplenia or polysplenia) (Q20.6)
- Q89.01 Asplenia (congenital)
- Q89.09 Congenital malformations of spleen
- Congenital splenomegaly
- Q89.1 Congenital malformations of adrenal gland
- Excludes1: adrenogenital disorders (E25.-)
- congenital adrenal hyperplasia (E25.0)
- Excludes1: adrenogenital disorders (E25.-)
- Q89.2 Congenital malformations of other endocrine glands
- Congenital malformation of parathyroid or thyroid gland
- Persistent thyroglossal duct
- Thyroglossal cyst
- Excludes1: congenital goiter (E03.0)
- congenital hypothyroidism (E03.1)
- Q89.3 Situs inversus
- Dextrocardia with situs inversus
- Mirror-image atrial arrangement with situs inversus
- Situs inversus or transversus abdominalis
- Situs inversus or transversus thoracis
- Transposition of abdominal viscera
- Transposition of thoracic viscera
- Excludes1: dextrocardia NOS (Q24.0)
- Q89.4 Conjoined twins
- Craniopagus
- Dicephaly
- Pygopagus
- Thoracopagus
- Q89.7 Multiple congenital malformations, not elsewhere classified
- Multiple congenital anomalies NOS
- Multiple congenital deformities NOS
- Excludes1: congenital malformation syndromes affecting multiple systems (Q87.-)
- Q89.8 Other specified congenital malformations
- Use additional code(s) to identify all associated manifestations
- Q89.9 Congenital malformation, unspecified
- Congenital anomaly NOS
- Congenital deformity NOS
Chromosomal abnormalities, not elsewhere classified (Q90-Q99)
- Excludes2: mitochondrial metabolic disorders (E88.3-)
Q90 Down syndrome
- Use